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Homo sapiens (human) The citric acid (TCA) cycle and respiratory electron transport (provided by Reactome)

170 gene

The longest variant of each gene is displayed. Click the see gene variants link to see all gene variants.


Gene Symbol Full Name
UQCRH ubiquinol-cytochrome c reductase hinge protein
COX4I1 cytochrome c oxidase subunit 4I1
DLAT dihydrolipoamide S-acetyltransferase
IDH3A isocitrate dehydrogenase 3 (NAD(+)) alpha
MIR4691 microRNA 4691
MIR6787 microRNA 6787
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
ATP5PD ATP synthase peripheral stalk subunit d
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
NDUFAF3 NADH:ubiquinone oxidoreductase complex assembly factor 3
COX18 COX18, cytochrome c oxidase assembly factor
L2HGDH L-2-hydroxyglutarate dehydrogenase
TACO1 translational activator of cytochrome c oxidase I
NDUFS5 NADH:ubiquinone oxidoreductase subunit S5
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
SLC25A14 solute carrier family 25 member 14
TIMMDC1 translocase of inner mitochondrial membrane domain containing 1
MPC1 mitochondrial pyruvate carrier 1
COX7C cytochrome c oxidase subunit 7C
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
LDHAL6A lactate dehydrogenase A like 6A
ATP5MF ATP synthase membrane subunit f
ATP6 ATP synthase F0 subunit 6
LRPPRC leucine rich pentatricopeptide repeat containing
COX8A cytochrome c oxidase subunit 8A
UQCRQ ubiquinol-cytochrome c reductase complex III subunit VII
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
COX11 COX11, cytochrome c oxidase copper chaperone
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
MDH2 malate dehydrogenase 2
PDK1 pyruvate dehydrogenase kinase 1
COX7B cytochrome c oxidase subunit 7B
COX6C cytochrome c oxidase subunit 6C
DLST dihydrolipoamide S-succinyltransferase
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
ATP5F1E ATP synthase F1 subunit epsilon
ETFA electron transfer flavoprotein alpha subunit
ATP5MG ATP synthase membrane subunit g
SLC16A3 solute carrier family 16 member 3
SDHC succinate dehydrogenase complex subunit C
ETFB electron transfer flavoprotein beta subunit
ND2 MTND2
ND5 NADH dehydrogenase, subunit 5 (complex I)
DLD dihydrolipoamide dehydrogenase
NDUFA4 NDUFA4, mitochondrial complex associated
ATP5PO ATP synthase peripheral stalk subunit OSCP
ATP5PF ATP synthase peripheral stalk subunit F6
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
HAGH hydroxyacylglutathione hydrolase
SURF1 SURF1, cytochrome c oxidase assembly factor
ACAD9 acyl-CoA dehydrogenase family member 9
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
RXRA retinoid X receptor alpha
LDHB lactate dehydrogenase B
SLC25A27 solute carrier family 25 member 27
GLO1 glyoxalase I
MPC2 mitochondrial pyruvate carrier 2
OGDH oxoglutarate dehydrogenase
NNT nicotinamide nucleotide transhydrogenase
UCP3 uncoupling protein 3
COX5A cytochrome c oxidase subunit 5A
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
NDUFA11 NADH:ubiquinone oxidoreductase subunit A11
NDUFC1 NADH:ubiquinone oxidoreductase subunit C1
COX1 cytochrome c oxidase subunit I
CYTB cytochrome b
ND1 NADH dehydrogenase, subunit 1 (complex I)
BSG basigin (Ok blood group)
COQ10A coenzyme Q10A
NDUFB3 NADH:ubiquinone oxidoreductase subunit B3
COX6A1 cytochrome c oxidase subunit 6A1
ECSIT ECSIT signalling integrator
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
LDHC lactate dehydrogenase C
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
ATP5MC1 ATP synthase membrane subunit c locus 1
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
TMEM126B transmembrane protein 126B
PPARD peroxisome proliferator activated receptor delta
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
NDUFAF7 NADH:ubiquinone oxidoreductase complex assembly factor 7
NDUFB7 NADH:ubiquinone oxidoreductase subunit B7
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
SCO1 SCO1, cytochrome c oxidase assembly protein
ATP5F1C ATP synthase F1 subunit gamma
SLC16A8 solute carrier family 16 member 8
COX7A2L cytochrome c oxidase subunit 7A2 like
PDP1 pyruvate dehyrogenase phosphatase catalytic subunit 1
ETFDH electron transfer flavoprotein dehydrogenase
NUBPL nucleotide binding protein like
D2HGDH D-2-hydroxyglutarate dehydrogenase
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
CYCS cytochrome c, somatic
PDHB pyruvate dehydrogenase E1 beta subunit
SLC16A1 solute carrier family 16 member 1
IDH3G isocitrate dehydrogenase 3 (NAD(+)) gamma
1 2
ORF