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Homo sapiens (human) Branched-chain amino acid catabolism (provided by Reactome)

24 gene

The longest variant of each gene is displayed. Click the see gene variants link to see all gene variants.


Gene Symbol Full Name
TMLHE trimethyllysine hydroxylase, epsilon
ACAD8 acyl-CoA dehydrogenase family member 8
DLD dihydrolipoamide dehydrogenase
MIR6778 microRNA 6778
ALDH9A1 aldehyde dehydrogenase 9 family member A1
BCKDK branched chain ketoacid dehydrogenase kinase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
ALDH6A1 aldehyde dehydrogenase 6 family member A1
IVD isovaleryl-CoA dehydrogenase
MCCC2 methylcrotonoyl-CoA carboxylase 2
ACAT1 acetyl-CoA acetyltransferase 1
DBT dihydrolipoamide branched chain transacylase E2
AUH AU RNA binding methylglutaconyl-CoA hydratase
ACADSB acyl-CoA dehydrogenase short/branched chain
SHMT1 serine hydroxymethyltransferase 1
PPM1K protein phosphatase, Mg2+/Mn2+ dependent 1K
HIBADH 3-hydroxyisobutyrate dehydrogenase
BBOX1 gamma-butyrobetaine hydroxylase 1
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
MCCC1 methylcrotonoyl-CoA carboxylase 1
BCAT1 branched chain amino acid transaminase 1
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
HSD17B10 hydroxysteroid 17-beta dehydrogenase 10
BCAT2 branched chain amino acid transaminase 2
ORF