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ORF » Species Summary » Homo sapiens » Reactome » Branched-chain amino acid catabolism
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Browse by Letter Index, Genomic Locus
24 gene
The longest variant of each gene is displayed. Click the see gene variants link to see all gene variants.
| Gene Symbol | Full Name |
|---|---|
| TMLHE | trimethyllysine hydroxylase, epsilon |
| ACAD8 | acyl-CoA dehydrogenase family member 8 |
| DLD | dihydrolipoamide dehydrogenase |
| MIR6778 | microRNA 6778 |
| ALDH9A1 | aldehyde dehydrogenase 9 family member A1 |
| BCKDK | branched chain ketoacid dehydrogenase kinase |
| HIBCH | 3-hydroxyisobutyryl-CoA hydrolase |
| ALDH6A1 | aldehyde dehydrogenase 6 family member A1 |
| IVD | isovaleryl-CoA dehydrogenase |
| MCCC2 | methylcrotonoyl-CoA carboxylase 2 |
| ACAT1 | acetyl-CoA acetyltransferase 1 |
| DBT | dihydrolipoamide branched chain transacylase E2 |
| AUH | AU RNA binding methylglutaconyl-CoA hydratase |
| ACADSB | acyl-CoA dehydrogenase short/branched chain |
| SHMT1 | serine hydroxymethyltransferase 1 |
| PPM1K | protein phosphatase, Mg2+/Mn2+ dependent 1K |
| HIBADH | 3-hydroxyisobutyrate dehydrogenase |
| BBOX1 | gamma-butyrobetaine hydroxylase 1 |
| BCKDHB | branched chain keto acid dehydrogenase E1 subunit beta |
| MCCC1 | methylcrotonoyl-CoA carboxylase 1 |
| BCAT1 | branched chain amino acid transaminase 1 |
| BCKDHA | branched chain keto acid dehydrogenase E1, alpha polypeptide |
| HSD17B10 | hydroxysteroid 17-beta dehydrogenase 10 |
| BCAT2 | branched chain amino acid transaminase 2 |